Case Report

Two Cases with Familial Hemophagocytic Lymphohistiositosi


  • Pelin Zorlu
  • Şit Uçar
  • Ebru Arık Yılmaz
  • Neşe Yaralı

Received Date: 06.10.2013 Accepted Date: 04.11.2013 J Pediatr Res 2014;1(2):104-107

Hemophagocytic lymphohistiocytosis is a rare, life-threatening disorder characterized with uncontrolled activation of T-helper 1 lymphocytes and macrophages and over-release of inflammatory cytokines. In this paper, we presented two patients who admitted to our hospital due to abdomen swelling, pallidness, febrility, hepatosplenomegaly and pancytopenia and diagnosed as familial hemophagocytic lymphohistiocytosis.

Keywords: Familial hemophagocytic lymphohistiocytosis, infant, pancytopenia

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